Ventricular septal defect
ICD-10 Q21.0 · ICD-11 LA88.4

Treatment of VSD in Severe Pulmonary Arterial Hypertension or Eisenmenger Physiology with Exercise-Induced Desaturation

Patients with ventricular septal defect who have developed Eisenmenger physiology or severe pulmonary arterial hypertension (PVR ≥5 WU) and who desaturate on exercise represent a distinct clinical sub-population requiring a carefully defined management approach.

Clinical Scenario

This protocol applies to VSD with Eisenmenger physiology, or with severe pulmonary arterial hypertension (PVR ≥5 WU), where the patient presents with a fall in arterial oxygen saturation below 90% on exercise. In this setting, the presence of significant PAH fundamentally shapes the management pathway. The full structured protocol defines the evidence-based approach for this population.

References

DOI: 10.1093/eurheartj/ehaa554

VSD closure is not recommended in patients with Eisenmenger physiology and patients with severe PAH (PVR ≥5 WU) presenting with desaturation on exercise.

There are limited data available for a precise cut-off, but by clinical experience, this would be given by a fall of arterial oxygen saturation <90%.

View source ↗