Systemic mastocytosis
ICD-10 D47.0 · ICD-11 2A21.0

Treatment of Systemic Mastocytosis with Recurrent Hypotension

Patients with indolent or smoldering systemic mastocytosis who experience recurrent hypotension represent a distinct clinical situation requiring targeted symptom-focused management.

In indolent or smoldering systemic mastocytosis (ISM/SSM), recurrent hypotension reflects episodic mediator release. Treatment goals in this population are primarily directed toward anaphylaxis prevention and symptom control.
The structured protocol for this scenario involves a combination of histamine-receptor antagonists targeting both H1 and H2 pathways — but the specific selection, sequencing, and management algorithm go beyond what can be summarised here.
Full regimen detail, dosing guidance, and clinical decision points are available via the link below.
References

DOI: 10.1002/ajh.26962

Treatment goals for ISM patients are primarily directed toward anaphylaxis prevention/symptom control/osteoporosis treatment.

H1- and H2-antagonists

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