Synovial sarcoma
ICD-10 C49.9 · ICD-11 2B5A

Treatment of Synovial Sarcoma in Patients Younger Than 18 Years

Clinical Scenario

Synovial sarcoma occurring in a patient under 18 years of age is a distinct and uncommon presentation. The disease is rare in the pediatric population, making it difficult to conduct randomized pediatric-specific clinical trials. The optimal approach to treatment in this age group is now better defined, though it requires careful clinical judgement.

Treatment Approach

For relapsing synovial sarcoma in this age group, management includes a multimodal strategy combining surgical and systemic interventions — the full sequence, options, and structured regimen are detailed in the complete protocol.

Full regimen, sequencing, and clinical criteria are available via the structured protocol below.
Instant Access to Structured Evidence-Based Regimens
References

DOI: 10.1016/j.esmoop.2023.101618

The optimal approach to the treatment of SS in pediatric patients is now better defined.

The disease is rare in the pediatric population, making it difficult to conduct randomized pediatric SS-specific clinical trials.

Approaches to relapsing SS in children have included additional surgery, second-line chemotherapy (e.g. with ifosfamide combinations), and radiotherapy.

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