Among patients diagnosed with Short QT syndrome, those who have experienced an aborted cardiac arrest, documented spontaneous sustained ventricular tachycardia, or arrhythmic syncope represent a high-risk subgroup for whom structured, evidence-based management is essential.
Current evidence-based guidance supports a device-based intervention as the central strategy in this setting. The complete structured regimen — including specific indication criteria, procedural considerations, and the full decision pathway — is available in the full protocol.
DOI: 10.1093/eurheartj/ehac262
ICD implantation is recommended in patients with a diagnosis of SQTS who: (a) are survivors of an aborted CA and/or (b) have documented spontaneous sustained VT.
ICD implantation should be considered in SQTS patients with arrhythmic syncope.
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