Reversible posterior leukoencephalopathy syndrome
ICD-10 I67.8; I67.4 · ICD-11 8B22.Y.1

Treatment of PRES Without Hypertension When a Triggering Agent or Medical Disorder Is Involved

While most cases of posterior reversible encephalopathy syndrome (PRES) occur in the setting of elevated blood pressure, a clinically important subset presents without hypertension. In these patients, the driving factor is an associated medical disorder or an exogenous triggering agent — and recognising that distinction directly shapes management.

Clinical Scenario

This protocol covers PRES occurring without hypertension, where an associated medical disorder or a specific triggering agent is the precipitating cause. Identifying the underlying trigger is a necessary first step in this population before further management can be directed appropriately.

Treatment Approach (Partial Overview)

The central intervention is identification of the associated medical disorder or triggering agent. Where a precipitating agent is found — such as a chemotherapeutic drug — discontinuation or replacement of that agent is the key action.

The complete structured regimen, including full sequencing and additional interventions, is available through the link below.
Instant Access to Structured Evidence-Based Regimens
References

DOI: 10.1056/NEJMra2114482

In patients who have PRES without hypertension, it is necessary to identify associated medical disorders or triggering agents that are known to be associated with the condition (Tables 1 and 2).

Treatment of PRES is primarily directed at mitigation of hypertension, as discussed below; managing seizures, brain edema, and encephalopathy; or discontinuation or replacement of a precipitating agent (e.g., a chemotherapeutic drug).

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