Retinal hemangioblastoma
ICD-10 D31.2 · ICD-11 2F36.Y.1

Treatment of Retinal Hemangioblastoma with Juxtapapillary or Extrapapillary Retinal Vascular Proliferation

This protocol addresses retinal hemangioblastoma presenting with foci of juxtapapillary or extrapapillary retinal vascular proliferation — a distinct clinical scenario that requires careful management consideration.

Foci of juxtapapillary or extrapapillary retinal vascular proliferation can occur in association with retinal hemangioblastoma. These lesions are occasionally encountered in patients with VHL disease and may threaten central vision when they progress.
Management of progressing lesions may involve a surgical intervention targeting the vascular proliferation directly. The complete protocol — including patient selection, procedural details, and sequencing — is available via the structured regimen below.
References

DOI: 10.1097/IAE.0000000000002572

Foci of juxtapapillary or extrapapillary retinal vascular proliferation are occasionally present in patients with VHL disease.

Those lesions that progress to exert tractional effects on the macula or overgrow the fovea with effects on central vision can be removed at vitrectomy.

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