When pulmonic stenosis arises as a component of a complex congenital heart lesion rather than in isolation, its management is inseparable from the broader anatomical defect and requires a distinct clinical approach.
This protocol applies to patients with pulmonary stenosis occurring as part of complex congenital heart defects, including tetralogy of Fallot, complete atrioventricular canal, double outlet right ventricle, and univentricular heart. In these patients the pulmonary stenosis is an integral part of the underlying lesion and cannot be addressed in isolation.
Management centres on surgical intervention directed at the complex congenital lesion as a whole.