In low-grade B-cell primary pulmonary lymphoma of MALT type, the clinical approach is shaped by the extent and behaviour of disease. Bilateral pulmonary involvement, extrapulmonary spread, or relapse and progression define a specific presentation that requires a distinct management strategy.
This protocol addresses patients with low-grade B-cell primary pulmonary lymphoma (MALT type) who present with bilateral pulmonary involvement, extrapulmonary disease, or relapse and progression. Exclusive chemotherapy is generally used in this setting.
DOI: 10.1183/09031936.02.00404102
Exclusive chemotherapy is generally used for patients with bilateral or extrapulmonary involvement, relapse or progression.
Combination regimens, such as cyclophosphamide, adriamycin, oncovin and prednisone (CHOP), have not proven more effective than single-agent regimens with chloraminophene, cyclophosphamide, azathioprine or steroids.
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