Primary myelofibrosis
ICD-10 D47.1 · ICD-11 2A20.2

Treatment of Primary Myelofibrosis with Symptomatic Splenomegaly in Low-Risk Disease

This protocol covers the management of low-risk primary myelofibrosis in patients who present with symptomatic splenomegaly and/or significant disease-related symptoms requiring active treatment despite low-risk disease classification.

Clinical Scenario

The patient has primary myelofibrosis stratified as low-risk, with clinically meaningful splenomegaly and/or accompanying symptoms. Symptomatic burden in the setting of low-risk disease is the defining feature that indicates the need for intervention at this stage.

Treatment Approach — Partial Overview

In this setting, management is built around an established cytoreductive approach. Further options and the complete selection algorithm — including when clinical trial enrollment is appropriate — are detailed in the full protocol.

Treatment Goals

The clinical objective is meaningful improvement: control of cytosis (reduction of leukocytosis and/or thrombocytosis) and measurable reduction of splenomegaly.

Instant Access to Structured Evidence-Based Regimens
References

DOI: 10.1182/blood.2022017423

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