Pheochromocytoma
ICD-10 E27.5 · ICD-11 5A75

Pheochromocytoma in Paraganglioma: Next Step When α-Adrenergic Blockade Does Not Achieve Preoperative Blood Pressure Targets

Clinical scenario

A paraganglioma is a tumor derived from extra-adrenal chromaffin cells of the sympathetic paravertebral ganglia of the thorax, abdomen, and pelvis. When hormonally functional, it requires preoperative haemodynamic stabilisation before surgical resection — either open (the general preference) or laparoscopic in selected small, noninvasive tumors at surgically favourable locations.

Previous line: inadequate response

Initial preoperative blockade with α-adrenergic receptor blockers — with β-adrenergic receptor blockers added to control tachycardia — did not achieve the required haemodynamic targets: seated blood pressure below 130/80 mm Hg, standing systolic above 90 mm Hg, and heart rate of 60–70 bpm seated / 70–80 bpm standing.

This protocol addresses what to do next.

Next-step approach

When α-adrenergic blockade alone is insufficient, add-on therapy with a calcium channel blocker is among the strategies used to achieve further blood pressure control — with additional preoperative options available in the full protocol for cases that require more aggressive stabilisation before surgery.

Clinical goal

Target haemodynamic state before proceeding to surgery: blood pressure below 130/80 mm Hg seated and above 90 mm Hg systolic standing, with a heart rate of 60–70 bpm seated and 70–80 bpm standing.

References

DOI: 10.1210/jc.2014-1498
  • A paraganglioma is a tumor derived from extra-adrenal chromaffin cells of the sympathetic paravertebral ganglia of thorax, abdomen, and pelvis.
  • We suggest open resection for paragangliomas, but laparoscopic resection can be performed for small, noninvasive paragangliomas in surgically favorable locations.
  • Calcium channel blockers are the most often used add-on drug class to further improve blood pressure control in patients already treated with α-adrenergic receptor blockers.
  • Based on retrospective studies and institutional experience, a target blood pressure of less than 130/80 mm Hg while seated and greater than 90 mm Hg systolic while standing seems reasonable, with a target heart rate of 60–70 bpm seated and 70–80 bpm standing.
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