Nijmegen breakage syndrome
ICD-10 Q87.8 ICD-11 4A01.31.1

What Is the Treatment of Nijmegen Breakage Syndrome?

Treatment Approach

Chemotherapy is the primary modality in the treatment of Nijmegen breakage syndrome. The protocol addresses dosing strategy — including the use of full-dose or a dose-modified regimen — with escalation guided by individual tolerance.

The complete algorithm, specific agent selection, dosing thresholds, and sequencing are contained in the full structured protocol below.

Instant Access to Structured Evidence-Based Regimens

References

Full-dose chemotherapy is the most frequently applied method.

In previous studies, it was suggested to administer 80% of dose chemotherapy, particularly alkylating agents as cyclophosphamide, DNA topoisomerase II inhibitors, and antimetabolites such as methotrexate, and increase doses when well toleration is observed.

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