Multiple endocrine neoplasia type 2A
ICD-10 E31.8 · ICD-11 2F7A.0.2

Treatment of MEN Type 2A in Bilateral Pheochromocytomas of the Adrenal Glands

Clinical Scenario

This protocol addresses patients with Multiple endocrine neoplasia type 2A (MEN2A) presenting with bilateral pheochromocytomas of the adrenal glands — a recognised manifestation of this hereditary syndrome in which both adrenal glands are affected simultaneously.

Bilateral Adrenal Involvement

The bilateral nature of adrenal involvement carries specific perioperative implications that directly shape the management plan. Because both glands are involved, the surgical approach and its hormonal consequences require careful planning both before and after the procedure.

Treatment Approach (Overview)

The primary intervention involves surgical resection of the bilateral pheochromocytomas, with corticosteroid coverage required intraoperatively and in the postoperative period. The steps that follow resection — and the specific management of hormonal status thereafter — depend on the surgical outcome.

The complete protocol, including postoperative hormonal management and monitoring guidance, is available in the full structured regimen.

Instant Access to Structured Evidence-Based Regimens
References

DOI: 10.1089/thy.2014.0335

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