IgA nephropathy
ICD-10 N02.8 · ICD-11 MF8Y.1

What Is the First-Line Treatment for IgA Nephropathy?

IgA nephropathy (IgAN) carries a risk of progressive, potentially irreversible kidney function loss in a substantial proportion of patients. First-line management is structured around slowing that progression through renin-angiotensin system inhibition, adjunctive pharmacological options, lifestyle modification, and strict blood pressure control — guided by validated quantitative targets.

Treatment approach
The cornerstone of first-line therapy is an angiotensin-converting enzyme inhibitor (ACEi) or an angiotensin II receptor blocker (ARB) at the optimised, maximally tolerated dose, with guideline-supported adjunctive pharmacological and lifestyle interventions available for patients at risk of progressive kidney function loss. The complete agent selection, sequencing, and criteria for each adjunctive option are set out in the full protocol.
Treatment targets
  • Urine protein excretion < 0.5 g/d (ideally < 0.3 g/d)
  • Rate of kidney function loss < 1 ml/min/yr
  • Blood pressure ≤ 120/70 mm Hg
References
  • We recommend that all patients with IgAN be treated with an optimized maximally tolerated dose of either an angiotensin-converting enzyme inhibitor (ACEi) or an angiotensin II receptor blocker (ARB) (1B).
  • Control of blood pressure with a target of ≤120/70 mm Hg.
  • The treatment goal in patients with IgAN at risk of progressive loss of kidney function is to reduce the rate of loss of kidney function to the physiological state (i.e., <1 ml/min/yr for most adults) for the rest of the patient's life.
  • The only validated early biomarker to help guide clinical decision-making is urine protein excretion, which should be maintained at a minimum of <0.5 g/d (or equivalent), and ideally at <0.3 g/d (or equivalent), accepting that in some patients with extensive kidney scarring, this may not be possible and that multiple treatment strategies, including nonpharmacologic interventions, may be needed to achieve this.
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