Idiopathic pulmonary fibrosis
ICD-10 J84.1 · ICD-11 CB03.4

What is the treatment of acute exacerbation in idiopathic pulmonary fibrosis?

Clinical Scenario

Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive interstitial lung disease. Patients can experience acute exacerbations — sudden, clinically significant deteriorations superimposed on the underlying fibrotic process. These events require prompt, structured management.

Treatment Approach

The approach to an acute exacerbation of IPF involves a corticosteroid-based intervention. The complete regimen — including specific agent selection, sequencing, and monitoring parameters — is available in the full protocol.

Full prescribing details and the structured algorithm are behind the link below.

Instant Access to Structured Evidence-Based Regimens

References

Acute exacerbations may be treated with corticosteroids.

DOI: 10.1164/rccm.202206-1098ST

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