Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive interstitial lung disease. Patients can experience acute exacerbations — sudden, clinically significant deteriorations superimposed on the underlying fibrotic process. These events require prompt, structured management.
The approach to an acute exacerbation of IPF involves a corticosteroid-based intervention. The complete regimen — including specific agent selection, sequencing, and monitoring parameters — is available in the full protocol.
Acute exacerbations may be treated with corticosteroids.
DOI: 10.1164/rccm.202206-1098ST
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