Hypersensitivity pneumonitis
ICD-10 J67 · ICD-11 CA70

Treatment of Hypersensitivity Pneumonitis in Fibrotic HP with Severe or Progressive Disease

Clinical Scenario

This protocol applies to patients with hypersensitivity pneumonitis who have developed a fibrotic phenotype accompanied by severe lung function impairment or evidence of progressive disease — a presentation that calls for a structured treatment approach.

Specific Situation

In fibrotic hypersensitivity pneumonitis with severe or progressive lung involvement, immunosuppressive therapy may be considered as part of the clinical management strategy.

Treatment Approach

Management in this setting may involve corticosteroids, though their role in fibrotic HP warrants careful clinical evaluation. The complete structured regimen — including sequencing and further considerations for this presentation — is available via the full protocol.

Instant Access to Structured Evidence-Based Regimens

References

In cases of fibrotic HP and severe or progressive disease, immunosuppressive therapy may be considered.

HP may initially respond to corticosteroids, but there is little evidence that corticosteroids provide a long-term benefit or slow the progression of fibrotic HP.

DOI: 10.1183/16000617.0169-2021

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