Hereditary spinocerebellar ataxia
ICD-10 G11.9 · ICD-11 8A03.1Z

Treatment of Generalised Spasticity in Hereditary Spinocerebellar Ataxia When Physiotherapy Has Not Provided Complete Relief

Generalised spasticity is a recognised complication of hereditary spinocerebellar ataxia. When an initial course of physiotherapy does not produce full resolution of spasticity, a structured pharmacological step is indicated.

Clinical Context

Spasticity — increased muscle tone or hypertonia caused by upper motor neurone lesions — can lead to muscle stiffness, spasms, and pain. It has been described across multiple subtypes of hereditary spinocerebellar ataxia, including a number of autosomal dominant and autosomal recessive forms.

When Physiotherapy Was Not Enough

First-line physiotherapy — including patient and carer education in correct posture, appropriate muscle use, and avoidance of spasticity triggers — did not achieve complete reduction of spasticity. The protocol below addresses the next management step when this goal has not been met.

Next-Step Pharmacological Approach

The protocol specifies a sequence of oral anti-spasticity agents, each introduced at a low starting dose and titrated slowly. The selection and ordering of agents follows a defined tolerability-based sequence — the complete regimen is available in the full protocol.

References

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