Hereditary spinocerebellar ataxia can present with focal spasticity, particularly affecting small muscles. This specific clinical picture calls for a targeted, evidence-based management approach distinct from general ataxia care.
Clinical scenario: Focal spasticity — especially in small muscle groups — is a recognised complication in hereditary spinocerebellar ataxia and is supported by evidence from numerous well-controlled, randomised trials as a treatable target.
Focal spasticity, particularly in small muscles, is probably best treated with intramuscular botulinum toxin injections for which numerous well-controlled, randomized trials have shown benefit.
To treat focal spasticity, particularly in small muscles, refer to a specialised clinic for treatment with intramuscular botulinum toxin injections, followed by physiotherapy.
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