Goodpasture syndrome
ICD-10 M31.0 · ICD-11 MF85

Treating Goodpasture Syndrome When Cyclophosphamide Is Not Tolerated or Refused

In anti-GBM disease, standard first-line management typically incorporates cyclophosphamide. When patients are intolerant of cyclophosphamide or decline it, a structured alternative approach is needed. Case reports document successful outcomes in this specific patient group.

Clinical scenario

Anti-GBM disease with intolerance of, or refusal of, cyclophosphamide — for example due to its toxicity or patient preference. An alternative immunosuppressive agent can be substituted within an otherwise similar treatment framework.

Treatment approach

The regimen is built around plasma exchange and glucocorticoids, with a selected alternative immunosuppressive agent used in place of cyclophosphamide. Which agent, how it is used, and the full clinical algorithm are specified in the complete protocol.

Full regimen details are available in the structured protocol below.

Instant Access to Structured Evidence-Based Regimens

References

DOI: 10.1038/kisup.2012.27

Mycophenolate could be used instead of cyclophosphamide in patients who refuse cyclophosphamide or are intolerant of cyclophosphamide because of its toxicity.

There are several case reports of patients with anti-GBM disease who were successfully treated with mycophenolate or MPA instead of cyclophosphamide.

View source ↗