Bladder dysfunction, including urinary retention and persistently elevated post-void residual (PVR) volumes, is a recognised complication in individuals with Friedreich ataxia. When PVR exceeds 100 mL — or frank urinary retention is present — a structured, evidence-based management approach is indicated.
This protocol applies to individuals with Friedreich ataxia who present with urinary retention or a persistently elevated post-void residual volume in excess of 100 mL. A patient's neurological status and functional abilities are key factors in determining the appropriate management pathway.
A catheterization-based strategy underpins the management of this presentation. The full protocol specifies which approach applies under each clinical condition and what patient factors guide that selection — details available in the structured regimen below.
DOI: 10.1186/s13023-022-02568-3
In a patient with persistently elevated post void residual volumes in excess of 100 mL, clean intermittent self-catheterization is indicated.
We conditionally recommend individuals with Friedreich ataxia in urinary retention undergo intermittent catheterization prior to insertion of an indwelling catheter, with suitability for catheterization dependent on their neurological abilities.
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