Friedreich ataxia
ICD-10 G11.1 · ICD-11 8A03.10

Treatment of Friedreich Ataxia with Reduced Left Ventricular Ejection Fraction and Heart Failure

When Friedreich ataxia is complicated by heart failure with reduced left ventricular ejection fraction, both the neurological disease and the cardiac comorbidity must be addressed. This is a recognised cardiac complication of Friedreich ataxia that has direct bearing on medication selection and clinical management.

Clinical scenario: Friedreich ataxia in the setting of reduced left ventricular ejection fraction and heart failure. The cardiac comorbidity is the defining feature of this protocol and drives the treatment strategy.
Treatment approach (partial): The recommended approach involves guideline-directed medical therapy aligned with established major heart failure guidelines — specific medication classes and the full decision algorithm are detailed in the complete protocol.
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References

DOI: 10.1186/s13023-022-02568-3

We conditionally recommend treating individuals with Friedreich ataxia with a reduced left ventricular ejection fraction with medications according to current American Heart Association/American College of Cardiology heart failure guidelines (2013 & 2017 update)

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