Friedreich ataxia
ICD-10 G11.1 · ICD-11 8A03.10

Treatment of Friedreich Ataxia with Permanent, Persistent or Paroxysmal Atrial Fibrillation

In Friedreich ataxia, cardiac involvement is common and can manifest as atrial fibrillation — permanent, persistent or paroxysmal — as well as other atrial tachyarrhythmias. These arrhythmias introduce specific management requirements that differ from the general neurological care of the condition.

This protocol is indicated for individuals with Friedreich ataxia who have permanent, persistent or paroxysmal atrial fibrillation or atrial tachyarrhythmias, and defines the recommended cardiac approach for this sub-population.

Treatment Approach

The protocol addresses anticoagulation for individuals with atrial fibrillation, alongside a distinct cardiac management strategy for those with atrial tachyarrhythmias.

The complete regimen — including sequencing, full recommendations, and specific considerations — is available in the structured protocol below.
Instant Access to Structured Evidence-Based Regimens

References

  1. We conditionally recommend anticoagulation over no anticoagulation in individuals with Friedreich ataxia with permanent, persistent or paroxysmal atrial fibrillation
  2. We conditionally recommend attempts to maintain a normal cardiac rhythm over rate control in individuals with Friedreich ataxia and atrial tachyarrhythmias, and also recommend consideration of ablation for those who remain severely symptomatic due to a persistent atrial tachyarrhythmia or frequent paroxysms of an atrial tachyarrhythmia

DOI: 10.1186/s13023-022-02568-3

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