Treatment of Fibrous Dysplasia of Bone in Mazabraud Syndrome with Painful Intramuscular Myxomas

Clinical Scenario

This protocol addresses patients with fibrous dysplasia of bone presenting in the context of Mazabraud syndrome — a rare condition in which fibrous dysplasia of bone is accompanied by intramuscular myxomas. The specific situation covered here is when those intramuscular myxomas become symptomatic and painful, requiring active clinical management.

Condition Context

In Mazabraud syndrome, intramuscular myxomas are more often than not asymptomatic and require no intervention. The clinical decision point arises when myxomas become painful — at which stage targeted management is indicated.

Approach

When intramuscular myxomas in Mazabraud syndrome become painful, a surgical approach is considered. The full protocol details the specific surgical intervention, patient selection criteria, and clinical decision pathway — access it below.

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References

DOI: 10.1186/s13023-019-1102-9

More often than not myxomas of Mazabraud's syndrome are asymptomatic, and require no intervention.

However, surgical excision is recommended if they become painful.

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