Fibrous dysplasia of bone
ICD-10 M85.0 ICD-11 FB80.0.1

Treatment of Fibrous Dysplasia of Bone with Persistent Bone Pain in FGF-23-Mediated Hypophosphatemia

Clinical Scenario

This protocol addresses patients with fibrous dysplasia of bone who have concurrent FGF-23-mediated hypophosphatemia and are experiencing persistent moderate-to-severe bone pain that requires bisphosphonate therapy. The metabolic abnormality and the pain together define the management pathway.

Key Condition — Bone Pain

Persistent moderate-to-severe bone pain in this setting is the primary clinical driver. Before bisphosphonate therapy can be introduced, the underlying hypophosphatemia must first be corrected — an important sequencing requirement. Hypophosphatemia should be corrected as best as possible prior to initiating bisphosphonates.

Treatment Approach (Partial)

Management begins with an initial phase of hypophosphatemia correction using vitamin D analogues and phosphate supplementation — a prerequisite that must be established before any bisphosphonate can be started. The complete protocol, including the specific agents, required duration, monitoring criteria, and subsequent bisphosphonate selection, is detailed in the full structured regimen.

Clinical Goals

Serum phosphate corrected Bone pain improvement
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References

DOI: 10.1186/s13023-019-1102-9
  1. The first step in the pharmacological management of FD is to ensure supplementation (not correction) of hypophosphatemia if present (see above), and vitamin D repletion (according to national guidelines).
  2. Importantly, hypophosphatemia should be corrected as best a possible for least 6 months prior to initiating bisphosphonates.
  3. The dose of phosphate supplement should be titrated to maintain serum phosphate at the lower end or just below the normal laboratory reference range for serum phosphate.
  4. The aim of initial dosing is to establish whether bisphosphonates are effective in providing pain relief.
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