Fibrosarcoma
ICD-10 C49.9 · ICD-11 2B53&XH4EP1

Treatment of Localized Fibrosarcoma — Non-High-Grade (G1 or GX)

This protocol addresses patients with localized fibrosarcoma at a non-high-grade histological grade — specifically grade G1 (well-differentiated) or GX (grade not assessable). Surgery is the established standard of care for localized soft tissue sarcomas in this setting.

Management centres on a surgical procedure, with the specific technique determined by the tumour's anatomical localisation and characteristics. The full surgical strategy — including the recommended approach and margin requirements — is detailed in the structured regimen.

Histological tumour-free resection margins (R0)

Achieving an R0 resection is the defining surgical objective to minimise the risk of local recurrence.

References
DOI: 10.18632/oncotarget.20136
  • Surgery represents the standard therapy of localized soft tissue sarcomas.
  • The surgical procedure depends on the tumour localization, its size and grade of malignancy.
  • In case of intramuscular localized soft tissue tumours, the affected muscle compartment should be resected en-bloc as part of the so-called compartment resection.
  • If on the other hand the tumours do not reach the muscle origin, and its insertion, or in case of an extracompartmental growth, a wide resection should be performed.
  • If possible an R0, tumour margin-free, resection should be achieved in order to minimize the risk of local recurrences.
  • Even though a 2 cm margin is sometimes recommended, a generally valid safety margin has not yet been determined.
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