La quimioterapia es la modalidad principal en el tratamiento del síndrome de Nijmegen. El protocolo aborda la estrategia de dosificación — incluido el uso de dosis completa o un régimen con dosis modificada — con escalada guiada por la tolerancia individual.
Full-dose chemotherapy is the most frequently applied method.
In previous studies, it was suggested to administer 80% of dose chemotherapy, particularly alkylating agents as cyclophosphamide, DNA topoisomerase II inhibitors, and antimetabolites such as methotrexate, and increase doses when well toleration is observed.
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