This protocol addresses endomyocardial fibrosis occurring in the paediatric population where restrictive cardiomyopathy is present alongside evidence of myocardial ischaemia and episodes of syncope — a combination that significantly influences the management approach.
Children with restrictive cardiomyopathy who also demonstrate myocardial ischaemia and syncope represent a high-risk subset. These concurrent findings are central to the risk assessment and directly inform which interventions are appropriate in this setting.
The evidence supports consideration of an implantable device-based intervention in this paediatric scenario. The specific device, eligibility criteria, and the full structured decision pathway are detailed in the complete protocol — access it below.
DOI: 10.1093/eurheartj/ehad194
ICD implantation may be considered in children with RCM who have evidence of myocardial ischaemia and syncope.
View source ↗