Treatment of Dominant Optic Atrophy with Sensorineural Hearing Loss

This protocol applies to the syndromic form of dominant optic atrophy (DOA) presenting with concurrent sensorineural hearing loss (neurosensorial deafness) — a distinct sub-population in whom audiological impairment is part of the syndromic picture and requires targeted intervention.

Management of the hearing component in this syndromic presentation involves a device-based auditory intervention. The full structured protocol specifies the indication criteria, patient selection considerations, and the complete evidence-based regimen — details available via the link below.

The primary clinical target is marked improvement of audition, directly addressing the sensorineural hearing loss associated with this syndromic form of dominant optic atrophy.