Technically Inoperable CTEPH: What to Do When Medical Therapy Has Not Met Haemodynamic Targets

Clinical scenario

This protocol applies to patients with chronic thromboembolic pulmonary hypertension who are technically inoperable — fibrotic obstructions lie within pulmonary artery segments not surgically accessible.

Previous treatment — goals not achieved

When medical therapy for inoperable CTEPH — including riociguat (first-line), or alternatives such as macitentan, subcutaneous treprostinil, or off-label oral combination therapy — has failed to achieve the treatment targets: specifically, a good functional class (WHO-FC I–II) and/or normalisation of haemodynamics at rest confirmed at right heart catheterisation, escalation to the next step is warranted.

Next-step approach (partial overview)

An interventional, staged procedure targeting distal pulmonary artery obstructions is considered for patients whose anatomy is amenable to this technique. The complete protocol — covering patient selection, staging strategy, and session-level detail — is available in the structured regimen.

Full procedural protocol available below.

Treatment goals

The target is achieving a good functional class (WHO-FC I–II) and/or normalisation or near-normalisation of haemodynamics at rest, confirmed at right heart catheterisation 3–6 months post-procedure, alongside improvement in quality of life.

Instant Access to Structured Evidence-Based Regimens

References

DOI: 10.1093/eurheartj/ehac237

Riociguat is recommended for symptomatic patients with inoperable CTEPH or persistent/recurrent PH after PEA.

BPA is recommended in patients who are technically inoperable or have residual PH after PEA and distal obstructions amenable to BPA.

A staged interventional procedure with a limited number of dilated PA segments per session is preferred.

Most experts accept achieving a good functional class (WHO-FC I-II) and/or normalization or near normalization of haemodynamics at rest, obtained at RHC 3-6 months post-procedure (PEA or last BPA), and improvement in quality of life.

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