Chronic thromboembolic pulmonary hypertension
ICD-10 I27.2 · ICD-11 BB01.3

Treatment of CTEPH with Fibrotic Pulmonary Artery Obstructions Accessible by Surgery

In chronic thromboembolic pulmonary hypertension (CTEPH), when fibrotic obstructions within the pulmonary arteries are surgically accessible, the clinical pathway is well-defined and guides selection of the appropriate intervention.

Clinical Scenario

This protocol applies to patients with CTEPH who have fibrotic obstructions within the pulmonary arteries that are accessible by surgery — an operable presentation. The location and nature of the lesions make a surgical approach feasible and, per current evidence, the preferred strategy.

Treatment Approach

For this operable population, a specific surgical procedure targeting the pulmonary arteries bilaterally is the treatment of choice. The precise technique, operative steps, and full procedural requirements are detailed in the complete protocol.

Full regimen available via the link below.
Treatment Goals

The primary goals are achieving a good functional class (WHO-FC I–II) and normalization or near-normalization of resting haemodynamics. These are evaluated by right heart catheterisation 3–6 months after the procedure.

Instant Access to Structured Evidence-Based Regimens

References

DOI: 10.1093/eurheartj/ehac237 View source ↗