Treatment of Chondrosarcoma Presenting as Atypical Cartilaginous Tumour in the Appendicular Skeleton

This protocol applies to chondrosarcoma diagnosed as an atypical cartilaginous tumour (ACT) at an appendicular skeleton site. The WHO classifies these lesions as atypical cartilaginous tumours in the appendicular skeleton — distinct from grade 1 chondrosarcoma in axial sites such as the scapula, pelvis, or skull. In extremity ACTs, initial observation is an established management option.

Management involves a surgical approach. Grade progression may occur, particularly following local recurrence, which can shift the clinical decision toward surgical intervention. The full protocol outlines the specific indications and sequence for this scenario.