Carcinoid of appendix
ICD-10 D37.3 · ICD-11 2B81.2

Treatment of Carcinoid of Appendix: Appendiceal NET 1–2 cm with Tumor Size >15 mm, G2 Grading, or Lympho-Vascular Invasion

Appendiceal neuroendocrine tumors measuring 1–2 cm represent a clinically distinct group. When certain pathological features are present, management shifts toward a more extensive surgical approach.

Clinical Scenario

This protocol applies when an appendiceal neuroendocrine tumor measures 1–2 cm in diameter and one or more of the following high-risk features are identified: tumor size > 15 mm, grading G2 (WHO 2010), and/or lympho-vascular invasion. These features are associated with a non-negligible risk of lymph node involvement and indicate that simple appendectomy alone may not provide definitive management.

Treatment Approach (Overview)

When these high-risk features are confirmed, a surgical radicalization procedure is indicated. The full protocol details the specific operative approach and the extent of nodal management involved.

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References

DOI: 10.1007/s11864-023-01093-0

In our opinion, patients presenting tumor size > 15 mm, grading G2 (according to WHO 2010), and/or lympho-vascular invasion should be referred for radicalization with RHC.

The clinical management of a T2 (ENETS) or T1b (UICC/AJCC) NET (i.e., tumors with diameters > 1 cm but < 2 cm) is more controversial because lymph node or distant metastases are uncommon but possible, so definitive cure can be achieved with a RHC.