Managing primary Budd-Chiari syndrome in the paediatric population presents unique clinical challenges. Structured guidance is especially important here, as very little evidence exists to inform decision-making in children with this condition.
Primary Budd-Chiari syndrome in paediatric patients (children). This age group represents a distinct sub-population in which available evidence is markedly limited, underscoring the value of protocol-driven management.
When interventional management options are not feasible or have not been successful, a surgical transplantation-based approach may be indicated. The full protocol defines the conditions and pathway for this intervention.