Autoimmune hepatitis
ICD-10 K75.4 · ICD-11 DB96.0

Treatment of Autoimmune Hepatitis in the AIH/Primary Sclerosing Cholangitis Variant Syndrome

Clinical scenario

This protocol addresses patients presenting with the autoimmune hepatitis / primary sclerosing cholangitis (AIH/PSC) overlap variant syndrome — a distinct clinical entity that combines features of both conditions and requires a tailored treatment strategy.

The variant syndrome

The AIH/PSC variant represents an overlap between autoimmune hepatitis and primary sclerosing cholangitis. This population — both adult and paediatric — carries specific management considerations that differ from either condition treated in isolation.

Treatment approach

Current evidence supports a combination strategy involving immunosuppressive therapy alongside ursodeoxycholic acid (UDCA) for patients with this variant syndrome.

The specific agents, dosing regimen, tapering sequence, and additional options are detailed in the full structured protocol.

Instant Access to Structured Evidence-Based Regimens
References
DOI: 10.1016/j.jhep.2025.03.017
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