لمفومة الخلايا التائية الشبيهة بالتهاب الأنسجة الدهنية تحت الجلد مع متلازمة اللمفاوية النسيجية البلعمية الدموية — عندما لا يحقق علاج الخط الأول استجابةً

References

SPTCL with HLH, Systemic Disease, or High Tumor Burden (Widespread Subcutaneous Disease)

In cases complicated by HLH, treatment of HLH concurrently with treatment of lymphoma is recommended.

Patients with disease relapse (after a period of observation or maintenance therapy) should receive treatment with either the same regimen previously given or an alternate regimen that was not given as first-line therapy.

Patients who do not achieve an adequate response to first-line therapy may be given a different first-line therapy or the same therapy at a higher dose to achieve disease control.