LCH الرئوي أحادي الجهاز في مدخن بالغ عندما لا يُحسّن العلاج الجهازي وظائف الرئة

References

DOI: 10.1182/blood.2021014343

Single-system pulmonary | Isolated lung involvement (predominantly smoking related). Cessation of smoking, vaping, inhalation of marijuana or other substances is recommended as first-line therapy for single-system PLCH.

For patients who develop advanced single-system PLCH refractory to or ineligible for systemic treatments, lung transplantation referral should be undertaken. Patients with advanced single-system PLCH may be candidates for lung transplantation, although the disease may relapse in the transplanted lungs.