علاج مرض الهيموغلوبين H مع أزمة انحلال الدم الحادة

References

• A haemolytic crisis is considered a dominant clinical feature of α-thalassaemia, and it is characterized by acute worsening of anaemia, frequently in combination with jaundice and/or dark-coloured urine.
• An acute haemolytic crisis is a major complication in HbH disease that requires emergency management.
• Restore patient’s Hb to 80–90 g/L by red cell transfusion.
• During an acute haemolytic episode, blood transfusion should be provided to restore Hb to 80–90 g/L, along with adequate intravenous hydration.