علاج داء تخزين الغليكوجين النوع الخامس في انحلال العضلات الشديد مع بيلة الميوغلوبين

References

Patients with severe rhabdomyolysis should be treated with adequate fluid administration to prevent renal impairment or be put on dialysis if warranted.

However, it is important to take into account the fluid balance to avoid further complications such as hypervolaemia and acute pulmonary oedema.

Myoglobinuria due to rhabdomyolysis can produce ARF, but data from large cohorts of patients suggest that this emergency complication is a rare event in both GSD V and GSD VII.

Discharge criteria are contingent upon a lack of myoglobinuria and a return to baseline renal function (creatinine and glomerular filtration rate).