علاج داء تخزين الجليكوجين من النوع الأول لدى الرضع

References

DOI: 10.1038/gim.2014.128

GSD I most commonly presents as hypoglycemia and/or hepatomegaly in infants.

In infancy, a soy-based, sugar-free formula or a formula that is free of sucrose, fructose, and lactose is fed on demand every 2–3 hours.

The formula may be offered every 4 hours by mouth and/or by tube, or the formula may be infused continually at a rate to provide adequate glucose to maintain the BG level at more than 70 mg/dl or 4 mmol/l.

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