داء الجليكوجين النوع الأول: ماذا تفعل عندما تفشل الإدارة الغذائية في الحفاظ على سكر الدم

References

DOI: 10.1038/gim.2014.128

• Raw cornstarch (CS) has been used for the treatment of hypoglycemia in GSD I since the early 1980s.
• General guidelines for dosing CS include 1.6 g of CS per kilogram of body weight (ideal body weight) every 3–4 hours for young children, and 1.7–2.5 g CS/kg every 4–5 hours (sometimes 6 hours) for older children, adolescents, and adults.
• Some adults may eventually only require one dose of CS at bedtime to maintain their BG at more than 70 mg/dl or 4 mmol/l and to maintain their lactates at less than 2 mmol/l through the night.