رنح فريدرايش مع إخلاء مجرى الهواء المتعثر (PECF أقل من 270 لتر/دقيقة أو FVC أقل من 50% من المتوقع)

References

1. In individuals with Friedreich ataxia and impaired airway clearance (PECF < 270 L/min or FVC < 50% predicted), we suggest assisted coughing (mechanical/manual) be implemented to assist in airway clearance and reduce the prevalence of chest infections.
2. In people with respiratory weakness and restrictive lung disease with Friedreich ataxia, we conditionally recommend chest physiotherapy to improve respiratory function, reduce prevalence of chest infection, reduce dyspnea and improve airway clearance function.