علاج خلل التعظم الليفي العظمي مع إصابة الوجه والجمجمة والضعف الوظيفي

References

DOI: 10.1186/s13023-019-1102-9

• The goals of treatment are: a) Prevention of functional loss – especially hearing and vision; b) Arrest or reduction of physical disfigurement; c) Prevention of secondary deformity; d) Minimisation of long-term morbidity from CFFD and its treatment.
• If CFFD is identified at baseline or at subsequent monitoring evaluations, the patient should be referred for a formal assessment to a craniofacial service with experience in the care of patients with CFFD.
• Treatment options include: burring of the lesion to reduce bulk and achieve symmetry; subtotal excision and reconstruction; complete excision of the lesion and reconstruction of the calvarial defect.
• Advanced imaging techniques and 3-dimensional analysis of scans together with virtual surgical planning and computer-aided manufacturing and design of patient-specific implants should be regarded as the standard of care in surgery of FD of the craniofacial skeleton.
• Simple curettage is not recommended as it is ineffective and may increase the risk of complications.