علاج الورم الليفي التكاثري في داء السلائل الغدية العائلي عندما لا تكون المراقبة الفعالة كافية بعد الآن

References

DOI: 10.1001/jamaoncol.2024.1805

Patients with mesenteric DT, whose further progression or residual disease after medical therapy completion would result in bowel complications, should also be considered for surgical resection.

For nonmesenteric DT, in cases of progression on medical treatment or active surveillance, surgery may be discussed in the multidisciplinary team when morbidity of resection is limited or when further progression or residual disease after therapy completion would result in bowel complications in cases of sporadic mesenteric DTs.

In sporadic mesenteric DT cases with complications, such as bleeding, obstruction, or perforation, surgery plays a critical role.

The consensus of the Desmoid Tumor Working Group was that for most of the available treatments, a course of at least 6 months is required (provided there is absence of frank progression) prior to assessing effectiveness.

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