Severe or Very Severe Aplastic Anaemia After First-Line Immunosuppression Failure — Patient Over 40 or No Matched Sibling Donor

This protocol applies to patients with acquired severe or very severe aplastic anaemia (SAA/VSAA) who have not achieved an adequate haematological response after a first course of immunosuppressive therapy, and who either have no HLA-matched sibling donor available or are over 40 years of age with a matched sibling.

Why This Protocol Is Triggered

First-line treatment with horse anti-thymocyte globulin, ciclosporin, and eltrombopag did not achieve the required response by 6 months: transfusion independence, or a complete response defined by haemoglobin normal for age and gender, neutrophils above 1.5 × 10&sup9;/L, and platelets above 150 × 10&sup9;/L.

Clinical Scenario

Acquired SAA or VSAA in patients with no available HLA-matched sibling donor, or — when a matched sibling is present — in patients aged over 40 years. Patients between 40 and 50 years with a matched sibling may require individual evaluation based on performance status, comorbidities, and centre expertise.

Salvage Approach — Partial Overview

Salvage therapy in this setting may involve transplant-based or non-transplant pathways, chosen based on donor availability and individual patient eligibility — full selection criteria, sequencing, and treatment details are in the complete protocol.

Instant Access to Structured Evidence-Based Regimens

References

DOI: 10.1111/bjh.19236

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