Anti-NMDA-receptor encephalitis
ICD-10 G04.8 · ICD-11 8E4A.0.3

Relapse of NMDA Receptor Antibody Encephalitis in Children Under 18

Clinical Scenario

This protocol addresses children younger than 18 years who experience a relapse of NMDA receptor antibody encephalitis — that is, the return of previously resolved symptoms and signs, or the appearance of new symptoms or signs, associated with a change in function.

Relapse is defined as: return of previously resolved symptoms and signs, or appearance of new symptoms or signs, associated with change in function, lasting more than 1 week (or shorter if associated with a change in safety), that cannot be explained by adverse reactions to current medications or intercurrent illness, after a period of stability or improvement of at least 1 month.
Treatment Approach

Current evidence supports first-line immunotherapy for all children with NMDA receptor antibody encephalitis relapse — including those who are already improving at the time of diagnosis. Combinations of first-line immunotherapy approaches are available and may be used as clinically indicated.

The full sequence, specific agents, and combination strategy are detailed in the complete protocol →

Instant Access to Structured Evidence-Based Regimens

References

  1. Return of previous resolved symptoms and signs, or appearance of new symptoms or signs, associated with change in function, lasting more than 1 wk (or shorter if associated with change in safety), that cannot be explained by adverse reactions to current medications or intercurrent illness, after a period of stability or improvement of at least 1 mo.
  2. First-line immunotherapy should be offered to all children with NMDARE relapse, even if they are improving at the time of diagnosis (i.e., late diagnosis or rapid improvement and remission). First-line immunotherapy and combinations can be used as per Table 2, 2.2.
DOI: 10.1212/NXI.0000000000001052 View source ↗