Acute promyelocytic leukemia
ICD-10 C92.4 · ICD-11 2A60.0&XH1A50

Treatment of Acute Promyelocytic Leukemia with WBC Above 10,000/ml (High-Risk APL)

Acute promyelocytic leukemia presenting with a white blood cell count above 10,000/ml defines the high-risk category. This threshold directly shapes the treatment strategy and is the basis for risk-stratified decision-making in APL.

Clinical scenario

APL is stratified by presenting WBC count. A WBC above 10,000/ml places patients in the high-risk group — a distinction most clinicians now use as the primary boundary between high risk and low/intermediate risk (≤10,000/ml). This classification is the defining feature of this protocol's target population.

Treatment approach (overview only)

The approach for this high-risk subset — including relapsed and refractory disease — centres on combination salvage strategies. Arsenic-based agents, used alone or combined with other agents, form a cornerstone of the regimens evaluated in this setting. The complete algorithm, specific combinations, and all dosing details are available in the full protocol.

Treatment goal: Regaining of molecular complete remission (PML-RARA negative).
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References

  1. In the era of ATRA, APL has been stratified into three categories of risk with regards to relapse-free survival (RFS): WBC >10,000/ml (high-risk), WBC ≤10,000 ml with platelet count ≤40,000/ml (intermediate-risk), and WBC ≤10,000/ml with platelet count >40,000/ml (low-risk).
  2. Today, most clinicians will categorize APL within two categories, high risk (>10,000/ml) and low/intermediate risk.
  3. The activity of ATO in relapsed disease has been demonstrated in multiple studies.
  4. The combination of ATO and other agents such as idarubicin and GO have also shown efficacy in regaining molecular CR.
DOI: 10.3389/fonc.2022.1062524
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