Acute lymphoblastic leukemia
ICD-10 C91.0 · ICD-11 2B33.3

Treatment of Relapsed or Primary Refractory Acute Lymphoblastic Leukemia

Acute lymphoblastic leukemia (ALL) that has either failed to respond to initial therapy (primary refractory) or has recurred after an initial response (relapsed) represents a distinct and challenging clinical scenario requiring a specific treatment approach.

This protocol addresses patients with relapsed or primary refractory ALL. Depending on protocol and subtype, 5% to 10% of patients will be primary refractory, and an additional 30% to 60% of patients will relapse.

Both groups — those whose disease never achieved remission and those who relapsed — carry a poor prognosis, and the clinical priority is achieving a new complete remission (CR).

The treatment strategy in this setting involves conventional salvage chemotherapy. The therapeutic goal is achievement of a new complete remission — attained in 20% to 40% of patients.

The full regimen, drug selection, sequencing, and supporting measures are detailed in the complete protocol →

References

Depending on protocol and subtype, 5% to 10% of patients will be primary refractory, and an additional 30% to 60% of patients will relapse.

Adult patients with R/R ALL have a poor prognosis with salvage chemotherapies.

A new CR is attained in 20% to 40% of patients depending on treatment line, but these remissions are in general not durable despite subsequent SCT.

DOI: 10.1182/blood.2023023568

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