Patients with acquired long QT syndrome who have experienced an aborted cardiac arrest represent a high-risk sub-population. This protocol addresses the structured management approach for LQTS with a history of sudden cardiac arrest.
This protocol applies to long QT syndrome patients with a history of aborted cardiac arrest — those who have survived a sudden cardiac arrest event. Device-based protection with an implantable cardioverter-defibrillator combined with beta-blocker therapy is recommended in this population.
In select patients meeting specific clinical criteria, a surgical procedure targeting the cardiac sympathetic nervous system forms part of the management strategy — the full eligibility criteria, sequencing, and complete regimen are available in the structured protocol below.