Acquired C1 inhibitor deficiency
ICD-10 D84.1 · ICD-11 4A00.15

Acquired Angioedema Secondary to C1-INH Deficiency with ≥2 Attacks per Week

Clinical Scenario

This protocol is indicated for patients with a confirmed diagnosis of acquired angioedema secondary to C1 esterase inhibitor deficiency (AAE-C1-INH) who are experiencing two or more angioedema attacks per week. This frequency of attacks defines a specific management category within AAE-C1-INH.

Qualifying Conditions

AAE-C1-INH Confirmed diagnosis of acquired angioedema secondary to C1 esterase inhibitor deficiency, with an attack burden of two or more episodes per week.

Treatment Approach

Management of this presentation involves an intravenous C1-esterase inhibitor as part of the structured regimen — the complete protocol, including selection criteria, full sequencing, and all clinical decision points, is available via the link below.

Partial summary only — full regimen details accessible in the protocol.

Instant Access to Structured Evidence-Based Regimens
References
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