Acquired C1 inhibitor deficiency
ICD-10 D84.1 · ICD-11 4A00.15

Treatment of Acquired Angioedema (AAE-C1-INH) During a Clinically Significant Acute Attack Requiring Admission or Injected Therapy

Acquired angioedema secondary to C1 esterase inhibitor deficiency (AAE-C1-INH) can produce acute attacks that are potentially life-threatening or severely disabling. When an attack meets the threshold for clinical significance, a specific evidence-based intervention is indicated.

Clinical Scenario

The patient carries a confirmed diagnosis of AAE-C1-INH and is presenting with a clinically significant acute attack — one that is either potentially life-threatening because it affects the head or neck, or causes pain or disability sufficient to prevent the patient from continuing normal activities. Clinical and risk assessment has determined that admission and injected treatment are required.

Treatment Approach (partial overview)

Acute management centres on specific injectable agents; available options include both a bradykinin-receptor–targeted agent and an intravenous C1-esterase inhibitor replacement product. The complete protocol specifies how to choose between them, guidance on product selection (including recombinant versus plasma-derived preparations), and the full decision algorithm — all available via the link below.

Instant Access to Structured Evidence-Based Regimens

References

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